Named after a John Susac in 1975, this condition comprises retinal arterial occlusion, sensorineural deafness and encephalopathy. Patients may present with speech impairment, headaches and migraines, hearing loss and reduced vision. It may be confused with multiple sclerosis and typically occurs in young women.
No abnormal features are found on ocular examination, but fluorescein angiography demonstrates focal nonperfused retinal arterioles wtih hyperfluorescant walls. When indocyanine angiography has been done, the choroidal circulation has been demonstrated to be normal.